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Antigenic Specificity | ALDH5A1, Human |
Clone | AT17F5 |
Host Species | Mouse |
Reactive Species | human |
Isotype | IgG2a kappa |
Format | Protein A purified |
Size | 50ul, 100ul |
Concentration | 1mg/ml (determined by BCA assay) |
Applications | ELISA,WB,ICC/IF |
Reviews / Ratings | If you have used this antibody, please help fellow researchers by submitting reviews to pAbmAbs and antYbuddY. |
Description | This protein belongs to the aldehyde dehydrogenase family of proteins. This gene encodes a mitochondrial NAD+-dependent succinic semialdehyde dehydrogenase. A deficiency of this enzyme, known as 4-hydroxybutyricaciduria, is a rare inborn error in the metabolism of the neurotransmitter gamma-aminobutyric acid (GABA). In response to the defect, physiologic fluids from patients accumulate GHB, a compound with numerous neuromodulatory properties. Two transcript variants encoding distinct isoforms have been identified for this gene. |
Immunogen | Recombinant human ALDH5A1 (48-535aa) purified from E. coli |
Other Names | Succinate-semialdehyde dehydrogenase mitochondrial, SSADH, SSDH, Succinate-semialdehyde dehydrogenase, mitochondrial |
Gene, Accession # | NCBI: NP_001071, UniProt: P51649 |
Catalog # | ATGA0398 |
Price | $170, $290 |
Order / More Info | ALDH5A1, Human Antibody from NKMAX Co. Ltd. |
Product Specific References | n/a |